Congenital aniridia is relatively rare familial condition which is transmitted by an autosomal dominant trait. Aniridia is characterized by reduction of the iris and visible only when the anterior chamber angle is examined with slit lamp or
gonioscope.
Associated conditions with aniridia are cataract, lens dislocation, congenial ocular nystagmus, absence of normal fovea centralis, strabismus, glaucoma etc.
The authors experienced a case of 7year old male patient who had familial aniridia in two generation combined with nystagmus, lens dislocation, divergence excess type of exodeviation. Both lateral rectus recession was performed in exodeviated
congenital
aniridia with satisfactory result. The authors report this case with the review of literatures.
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